Epididymal Lymphangioma: An Atypical Case of Scrotal Swelling and Literature Review

Lymphangioma of the epididymis is a rare condition that originates from the sequestration of lymphatic tissue, leading to a lack of normal communication with the lymphatic system. It consists of unilocular or multilocular lymphatic cysts lined by a single layer of endothelium. This benign tumor is typically identified at birth, during childhood, early adolescence, and occasionally in adulthood, with the most common locations being the head, neck, and axilla. Lymphangioma of the epididymis is exceptionally uncommon, with the first reported case by Thompson in 1936. Only six cases of cystic lymphangioma of the epididymis in adults have been documented in the English literature to date.

Here, we present an atypical case involving a 35-year-old male with a huge benign cystic lymphangioma of the right epididymis, manifesting as a painless inguinoscrotal cystic mass extending up to umbilicus. A complete surgical excision was performed, to minimize the risk of recurrence.